Aortic Root Surgery in Marfan Syndrome
Keimyung University, Daegu, Korea, Republic of.
OBJECTIVE: Marfan syndrome is characterized by variable clinical manifestations, including skeletal, ocular, and cardiovascular abnormalities. Ascending aortic aneurysm ensuing dissection and rupture is the main life-threatening cardiovascular manifestations of Marfan syndrome. The aim of this study was to evaluate the operative results of patients with Marfan syndrome who underwent aortic root surgery
METHODS: Author retrospectively analyzed the data of 72 operations in 68 patients with Marfan syndrome who underwent aortic root surgery between Jan. 1996 and Aug. 2014.
RESULTS: Among the 68 patients, 16 patients (24%) had family history. There were 55 patients who had aortic root replacement surgery, 17 patients who had aortic root sparing surgery. Aortic root replacement surgery included 52 button type aortic root replacement, and 3 Cabrol type aortic root replacement. Aortic root sparing procedure included 7 root remodeling procedure , 9 root reimplantation procedure and 1 other type aortic root sparing procedure. Combined procedures included 9 mitral valve surgery, 8 coronary artery bypass surgery, 2 total aortic arch replacement and 1 femorofemoral bypass surgery. There were one early death. During follow up period, 4 patients needed redo aortic root surgery included 3 recurrent aortic regurgitation and 1 endocarditis
CONCLUSIONS: Aortic root surgery in Marfan patients can be performed with good results. Close follow up of patients undergoing surgery is important.
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